Anti-HEXA Antibody |产品详情|进口橙子视频旧款采购网

您好，欢迎来到橙子视频app安卓下载生物网站！请登录注册

我的订单 | 联系橙子视频app安卓下载 | 在线客服QQ：3012681483 | 客服电话：400-968-7988 | 工作时间：08:30-17:30

主营产品： ELISA91橙子视频、抗体、补体血清、兔补体、干扰素、小鼠测温仪、进口橙子视频旧款、Quidel代理、Swant代理、PBL Assay Science代理

网站首页产品中心代理品牌新闻资讯资源中心关于橙子视频app安卓下载

所在位置：首页 > 产品中心 > Antibodies > Antibodies产品

订购信息

上海橙子视频app安卓下载生物科技公司

Tel:400-968-7988 021-33779008

Anti-HEXA Antibody

品牌：Antibodies

货号：

规格：100µl

货期：

应用：

咨询客服

立即购买加入购物车

Anti-HEXA Antibody

商品详情参考文献相关资料

Overview

Name:	Anti-HEXA Antibody See all HEXA primary antibodies
Description:	Rabbit polyclonal antibody to HEXA
Specificity:	The antibody detects endogenous level of total HEXA protein.
Applications:	WB, IHC
Reactivity:	Human, Mouse, Rat
Immunogen:	Recombinant protein of human HEXA.
Host:	Rabbit
Clonality:	Polyclonal
Conjugate:	Unconjugated
Purification:	Antibodies were purified by affinity purification using immunogen.
Concentration:	1.0mg / ml
Formulation:	Supplied at 1.0mg / mL in phosphate buffered saline (without Mg2+ and Ca2+), pH 7.4, 150mM NaCl, 0.02% sodium azide and 50% glycerol.
Storage:	Store at -20?C

Target

Function:	Responsible for the degradation of GM2 gangliosesides, and a variety of other molecules containing terminal N-acetyl hexosamines, in the brain and other tissues. The form B is active against certain oligosaccharides. The form S has no measurable activity.
Involvement in Disease:	GM2-gangliosesidosis 1: An autosomal recessive lysosomal storage disease marked by the accumulation of GM2 gangliosesides in the neuronal cells. It is characterized by GM2 gangliosesides accumulation in the absence of HEXA activity, leading to neurodegeneration and, in the infantile form, death in early childhood. It exists in several forms: infantile (most common and most severe), juvenile and ***** (late-onset).
Sequence Similarities:	Belongs to the glycosyl hydrolase 20 family.
Post-Translational Modification:	N-linked glycan at Asn-115 consists of Man(3)-GlcNAc(2).
Cellular locations:	Lysosome.
Database Links:	Entrez Gene: 3073?Human Entrez Gene: 15211?Mouse Entrez Gene: 300757?Rat Omim: 606869?Human SwissProt: P06865?Human SwissProt: P29416?Mouse SwissProt: Q641X3?Rat Unigene: 604479?Human Unigene: 709495?Human Unigene: 2284?Mouse Unigene: 92939?Rat
Synonyms:	Beta hexosaminidase alpha chain precursor Antibody Beta hexosaminidase subunit alpha Antibody Beta N acetylhexosaminidase Antibody Beta N acetylhexosaminidase subunit alpha Antibody Beta-hexosaminidase A Antibody Beta-hexosaminidase subunit alpha Antibody Beta-N-acetylhexosaminidase subunit alpha Antibody HEXA Antibody HEXA_HUMAN Antibody Hexosaminidase A Antibody Hexosaminidase A (alpha polypeptide) Antibody Hexosaminidase A alpha polypeptide Antibody Hexosaminidase subunit A Antibody MGC99608 Antibody N acetyl beta glucosaminidase Antibody N acetyl beta glucosaminidase subunit alpha Antibody N-acetyl-beta-glucosaminidase subunit alpha Antibody TSD Antibody
Information:	Target information shown above is from the UniProt Consortium.